Long survival after resection for lung metastasis of malignant peripheral nerve sheath tumor in neurofibromatosis 1.

نویسندگان

  • Katsuhiko Shimizu
  • Riki Okita
  • Yoko Uchida
  • Jun Hihara
چکیده

A 31-year-old man with neurofibromatosis 1 (NF1) was admitted for the treatment of solitary lung tumor. Nine months earlier he had undergone a large resection for malignant peripheral nerve sheath tumors (MPNSTs) in his back. Surgical resection of the right lower lobe was performed, and the tumor was pathologically diagnosed as a metastasis of MPNST. The survival of patients with pulmonary metastasis of MPNST is extremely poor, especially of those with NF1, but this patient has survived 5 years without recurrence. Based on our knowledge of the literature, a 5-year survival is extremely rare, and select patients have benefited from a resection of pulmonary metastasis.

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عنوان ژورنال:
  • Annals of thoracic and cardiovascular surgery : official journal of the Association of Thoracic and Cardiovascular Surgeons of Asia

دوره 14 5  شماره 

صفحات  -

تاریخ انتشار 2008